Iga Pemphigus

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2021-01-18
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IgA pemphigus is a subtype of pemphigus with two distinct forms:

  • Subcorneal pustular dermatosis (also known as Sneddon–Wilkinson disease and pustulosis subcornealis) is skin condition that is a rare, chronic, recurrent, pustular eruption characterized histopathologically by subcorneal pustules that contain abundant neutrophils.:203 This is distinct from and not to be confused with subcorneal pustular dermatosis type of IgA pemphigus. Sneddon's syndrome, also known as Ehrmann-Sneddon syndrome, is also a different syndrome.
  • Intraepidermal neutrophilic IgA dermatosis is characterized histologically by intraepidermal bullae with neutrophils, some eosinophils, and acantholysis.:465

History

Early descriptions were made by Darrell Wilkinson, a British dermatologist.

See also

  • Pemphigus
  • List of cutaneous conditions
  • List of conditions caused by problems with junctional proteins
  • List of immunofluorescence findings for autoimmune bullous conditions