Ependymoma
Watchlist
Retrieved
2021-01-23
Source
Trials
—
Genes
RELA,
C11orf95,
EPHB2,
GDNF,
RTBDN,
BCL7C,
RAB3A,
ZNF668,
TP53,
NF2,
IDH1,
APC,
TSC2,
ERBB2,
MSH2,
MSH6,
IFNG,
MLH1,
SETBP1,
TSC1,
PMS2,
CDKN2A,
YAP1,
EGFR,
MME,
VEGFA,
OLIG2,
MKI67,
MGMT,
MDM2
RELA,
C11orf95,
EPHB2,
GDNF,
RTBDN,
BCL7C,
RAB3A,
ZNF668,
TP53,
NF2,
IDH1,
APC,
TSC2,
ERBB2,
MSH2,
MSH6,
IFNG,
MLH1,
SETBP1,
TSC1,
PMS2,
CDKN2A,
YAP1,
EGFR,
MME,
VEGFA,
OLIG2,
MKI67,
MGMT,
MDM2,
MIB1,
TP73,
TTR,
PTEN,
MYCN,
TNC,
MAMLD1,
L1CAM,
EPB41L3,
MEN1,
FGFR1,
NOTCH1,
H3P10,
EZHIP,
NCL,
ANXA1,
CD274,
ATRX,
SST,
CCND1,
DAPK1,
RASSF1,
MIR17,
NES,
CDKN2B,
MUC1,
CD44,
TNFRSF10C,
PROM1,
ABCB1,
PDGFRA,
SLC9A3R1,
IL6,
KIT,
CASP8,
FGFR3,
DCX,
HIC1,
SOX10,
SMARCB1,
ARHGAP24,
ETFA,
GFAP,
TNFSF10,
SYP,
GATD3A,
LINC00899,
MIR146B,
IL18R1,
ABCC8,
ZNF148,
KRT75,
MIR449A,
STC1,
PSCA,
CLDN5,
TRERNA1,
TERT,
LOC110806263,
TPR,
TIMP3,
LINC02210-CRHR1,
THBS1,
ABCG2,
SIK1B,
TSPAN4,
TWIST1,
UBE2N,
GATD3B,
TDG,
VEGFB,
ZEB1,
SYT1,
AZIN2,
MVP,
MIR10B,
DNAJC15,
ZMYND10,
SHC3,
TET2,
FBXW7,
BEX1,
MIR10A,
MIR100,
LINC01194,
HES4,
GADL1,
ZFHX4,
SIK1,
ARMC9,
ESX1,
C1orf194,
TP53INP1,
GLS2,
CBY1,
MIR330,
KIF4A,
EBI3,
MIR135B,
AKR1A1,
MIR34C,
TUBB3,
MIR29A,
LRIG3,
HOXB13,
MIR24-1,
IPO7,
MIR221,
MIR19A,
MXD4,
MIR181C,
MIR15A,
DICER1,
HEY2,
STAT3,
JAG1,
SPINK1,
EPO,
MECOM,
EZH2,
FCGR1A,
FHIT,
FOXJ1,
FLT1,
GH1,
GNAO1,
HOXA9,
HES1,
HTC2,
HTR1B,
IDH2,
IGF2,
IGFBP2,
IGFBP3,
IGFBP5,
IL1R1,
CXCL8,
JAG2,
JAK2,
ERCC1,
EPB41,
SOX11,
S1PR3,
AQP1,
ASAH1,
BDNF,
BRAF,
CALCA,
CALCR,
CALR,
CAPS,
CAV1,
RUNX1,
CD34,
CD38,
CD151,
CDK6,
CHI3L1,
CCR7,
CRHR1,
CTNNB1,
DAXX,
DRD1,
DRD2,
KDR,
LAMA2,
RPSA,
STMN1,
PTPRS,
RAC2,
RAD51,
ALK,
RBL2,
RFX3,
RRM1,
S100A1,
S100A2,
S100A4,
S100A6,
S100A12,
S100B,
SHH,
SLC6A8,
SMN1,
SMN2,
SNCA,
SNCG,
SOX4,
SOX9,
PTPRA,
PTGS2,
PLG,
NFIC,
LRP1,
MAP2,
MDM4,
MET,
CD99,
ABCC1,
MSH3,
NELL2,
NF1,
NFKB1,
PIK3CG,
NGF,
OTX2,
PAX5,
PAX6,
PCNA,
PDGFRB,
PIK3CA,
PIK3CB,
PIK3CD,
RARB
Drugs
—
Registered!

Ependymoma is the most frequent intramedullary tumor in adults (but accounts for only 10-12% of pediatric central nervous system tumors), and can be benign or anaplastic. Ependymoma arise from the ependymal cells of the cerebral ventricles, corticle rests and central canal of the spinal cord, and manifest with variable symptoms such headache, vomiting, seizures, focal neurological signs and loss of vision and can cause obstructive hydrocephalus in some cases.